Epidemiology
A low-grade malignant tumor that typically affects the tibia (shinbone) in adolescents and young adults. A location in the front of the tibia in a young patient is a strong clue and requires distinguishing it from osteofibrous dysplasia.
Basic features
It can cause chronic pain, deformity, or swelling at the front of the leg, often with a long-standing history.
Usual treatment
The decisive treatment is wide resection with reconstruction (avoiding curettage, which increases recurrence), because it does not respond reliably to chemotherapy or radiotherapy.
Outcomes and prognosis
It is low-grade malignant: the prognosis is favorable with wide resection, but it can recur or metastasize late, so it requires long-term surveillance.
