Epidemiology
A rare fibrous tumor of children and adolescents, typically in the hands and feet. It tends to adhere to the aponeuroses and tendons of the hands or feet, which explains recurrences and local stiffness.
Basic features
It attaches to fascia, tendon, or aponeurosis and may contain calcifications that are visible on X-ray. It has a preference for the palms and the soles, and the calcifications tend to become more evident as the child grows.
Usual treatment
Resection is planned by balancing local control with preserving function in the digits or the foot.
Outcomes and prognosis
It can recur, especially in young children, but it does not usually metastasize.