Epidemiology
A rare intraosseous fibrous tumor, related in behavior to desmoid fibromatosis. It is benign under the microscope, but it behaves like a desmoid inside the bone: hearing "benign" here does not mean observation is enough.
Basic features
It is histologically benign but can destroy bone locally, cause pain, and compromise stability.
Usual treatment
Resection or extended curettage is preferred when feasible; the strategy depends on location and the expected morbidity.
Outcomes and prognosis
It does not metastasize, but local recurrence is frequent after simple curettage and lower after wide resection, so prolonged monitoring is recommended.
