Epidemiology
A rare vascular tumor of bone that can be multifocal and can affect young or middle-aged adults. When it affects more than one bone, the workup seeks to distinguish multifocality from disseminated disease.
Basic features
It can mimic infection, metastasis, or other vascular tumors, which is why a pathology-based diagnosis is important. Many cases show a rearrangement of the FOS or FOSB gene, useful to confirm it and to distinguish it from a malignant vascular tumor.
Usual treatment
It is managed with curettage, resection, embolization, or radiotherapy, depending on the number of lesions, the location, and the symptoms.
Outcomes and prognosis
It usually carries a low risk of metastasis, but it can recur or persist locally and requires individualized follow-up.
