Epidemiology
A rare soft-tissue sarcoma, more common in older adults, usually located deep in the thigh or pelvic girdle. Before surgery, it is confirmed that the tumor arises in soft tissue and does not correspond to extension from a nearby bone.
Basic features
It produces malignant osteoid without any connection to the neighboring bone, so imaging must confirm that it originates outside the bone.
Usual treatment
Treatment is based on wide resection; radiotherapy or chemotherapy are considered depending on size, grade, margins, and extent. Before chemotherapy starts it is worth discussing fertility preservation with the team, because some of these treatments can affect it and the options have to be raised beforehand.
Outcomes and prognosis
It carries a meaningful risk of local recurrence and metastasis and a guarded prognosis, so it needs close oncology follow-up.
