Epidemiology
A rare variant of osteosarcoma that arises on the surface of the bone and behaves like a high-grade tumor. Although it arises on the surface, its high grade requires staging and planning similar to other aggressive osteosarcomas.
Basic features
It can be confused with other surface tumors, so the correlation between imaging, biopsy, and the exact site is critical.
Usual treatment
It is treated with systemic chemotherapy and wide resection, similar to high-grade central osteosarcoma. Before chemotherapy starts it is worth discussing fertility preservation with the team, because some of these treatments can affect it and the options have to be raised beforehand.
Outcomes and prognosis
It behaves like a high-grade osteosarcoma: the prognosis depends on systemic control and on the margins, and it must not be managed as a low-grade surface lesion.
