Epidemiology
A rare superficial neoplasm of adults, described mainly in the limbs and subcutaneous tissue. The microscopic appearance can seem alarming, so review by expert pathology avoids overtreatment.
Basic features
It can show striking atypia under the microscope despite a relatively indolent clinical course.
Usual treatment
It is managed with complete removal and expert pathology review to distinguish it from more aggressive sarcomas.
Outcomes and prognosis
Recurrence and metastasis are uncommon, but follow-up is advised because of its rarity.
